The Catastrophic Antiphospholipid Antibody Syndrome: An Unusual Presentation of Spontaneous Acute Intracranial Haemorrhage
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چکیده
Background: Catastrophic Antiphospholipid syndrome (CAPS) is a scarcely understood entity with a high mortality approaching 50%The rapid deterioration is triggered by a deadly cytokine storm, which is difficult to recognize and almost impossible to treat in time. Various regimens have been advocated, which include administration of monoclonal anti-phospholipid antibodies and pulses of high dose methyl prednisolone. However, these treatment modalities are only effective if the disease is diagnosed early and instituted.
منابع مشابه
Catastrophic antiphospholipid antibody syndrome presenting as acute vascular occlusion in a young female patient.
Acquired thrombotic and thromboembolic disorders may be presented initially with symptoms and signs of acute ischaemia or organ dysfunction that will lead many of these patients to seek care in the emergency department. We report a case of a 19-year-old female patient who developed catastrophic antiphospholipid syndrome (CAPS syndrome or Asherson syndrome) 6 weeks post stillbirth with an initia...
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logic correlations of the antiphospholipid syndrome. Semin Arthritis Rheum 1995; 24:262-72. 2 Asherson RA. The catastrophic antiphospholipid syndrome. J Rheumatol 1992;19:508-12. 3 Asherson RA, Piette J-C. The catastrophic antiphospholipid syndrome 1996: acute multiorgan failure associated with antiphospholipid antibodies: a review of 31 patients. Lupus 1996;5:414-7. 4 Mazzucchelli R, Barbadill...
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